Journal of the Chinese Medical Association
Volume 70, Issue 1 , Pages 30-32, January 2007

An Adult with Aortic Arch Interruption Associated with Sinus Venosus Atrial Septal Defect and Partial Anomalous Pulmonary Venous Connection

  • Yu-Cheng Hsieh

      Affiliations

    • Cardiovascular Center, Taichung Veterans General Hospital, Taichung, Taipei, Taiwan, R.O.C.
    • Institute of Clinical Medicine and Cardiovascular Research Center, National Yang-Ming University School of Medicine, Taipei, Taiwan, R.O.C.
    • ,
  • Tsu-Juey Wu

      Affiliations

    • Cardiovascular Center, Taichung Veterans General Hospital, Taichung, Taipei, Taiwan, R.O.C.
    • Institute of Clinical Medicine and Cardiovascular Research Center, National Yang-Ming University School of Medicine, Taipei, Taiwan, R.O.C.
    • Corresponding Author InformationCorrespondence to: Dr Tsu-Juey Wu, Cardiovascular Center, Taichung Veterans General Hospital, 160, Section 3, Chung-Kang Road, Taichung 407, Taiwan, R.O.C.
    • ,
  • Kuo-Yang Wang

      Affiliations

    • Cardiovascular Center, Taichung Veterans General Hospital, Taichung, Taipei, Taiwan, R.O.C.
    • ,
  • Kae-Woei Liang

      Affiliations

    • Cardiovascular Center, Taichung Veterans General Hospital, Taichung, Taipei, Taiwan, R.O.C.
    • Institute of Clinical Medicine and Cardiovascular Research Center, National Yang-Ming University School of Medicine, Taipei, Taiwan, R.O.C.
    • ,
  • Wei-Wen Lin

      Affiliations

    • Cardiovascular Center, Taichung Veterans General Hospital, Taichung, Taipei, Taiwan, R.O.C.
    • ,
  • Ying-Tsung Chen

      Affiliations

    • Cardiovascular Center, Taichung Veterans General Hospital, Taichung, Taipei, Taiwan, R.O.C.
    • ,
  • Chih-Tai Ting

      Affiliations

    • Cardiovascular Center, Taichung Veterans General Hospital, Taichung, Taipei, Taiwan, R.O.C.
    • Institute of Clinical Medicine and Cardiovascular Research Center, National Yang-Ming University School of Medicine, Taipei, Taiwan, R.O.C.

Received 12 April 2006; received in revised form 18 August 2006

Article Outline

Interruption of the aortic arch is a rare and usually lethal congenital anomaly that is often associated with multiple cardiac malformations. Most neonates with aortic arch interruption perish once the ductus arteriosus closes after birth. However, sporadic cases have been reported to survive into adulthood uneventfully. Here, we report a 19-year-old male with a 3-month history of exertional dyspnea. A series of cardiovascular studies confirmed the presence of aortic arch interruption in conjunction with sinus venosus atrial septal defect and partial anomalous pulmonary venous connection. To the best of our knowledge, such an association has not been previously reported in adults.

Key Words:  atrial septal defect , interrupted aortic arch , partial anomalous pulmonary venous connection

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References 

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PII: S1726-4901(09)70297-7

doi:10.1016/S1726-4901(09)70297-7

Journal of the Chinese Medical Association
Volume 70, Issue 1 , Pages 30-32, January 2007

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